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KMID : 1033620220490030215
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Clinical and Experimental Reproductive Medicine
2022 Volume.49 No. 3 p.215 ~ p.218
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A case of congenital cloacal exstrophy/omphalocele-exstrophy-imperforate anus-spinal defects syndrome and a successful pregnancy
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Seat Mara
Boxwalla Munira
Hough Arielle
Goodwin Glenn
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Abstract
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Herein, we report an exceptionally rare case of a 25-year-old woman with cloacal exstrophy/omphalocele-exstrophy-imperforate anus-spinal defects (OEIS) syndrome achieving a viable pregnancy despite many gastrointestinal and genitourinary malformations and multiple respective corrective operations. The patient was born with two vaginas, two uteruses, four ovaries, an imperforate anus, a large omphalocele including bowel and bladder exstrophy, and diaphysis of the pubic rami. This patient is the only documented OEIS patient not to have tethered spinal cord as an anomaly, perhaps contributing to her successful pregnancy. After experiencing preeclampsia with severe features at 35 weeks, the baby was born via cesarean section.
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KEYWORD
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Cloacal exstrophy, Exstrophy epispadias complex, Exstrophy epispadias sequence, Exstrophy of cloaca, Imperforate anus and spinal defects, Omphalocele
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Listed journal information
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